The Journal of Thoracic and Cardiovascular Surgery
Volume 137, Issue 3 , Pages 538-542 , March 2009

Congenital supravalvar mitral ring: An underestimated anomaly

  • Alessandra Toscano, MD, PhD

      Affiliations

    • Department of Cardiology, Bambino Gesù Pediatric Hospital, Rome, Italy
    • ,
  • Luciano Pasquini, MD, FESC

      Affiliations

    • Department of Cardiology, Bambino Gesù Pediatric Hospital, Rome, Italy
    • Corresponding Author InformationAddress for reprints: Luciano Pasquini, MD, FESC, Department of Cardiology and Cardiothoracic Surgery, Bambino Gesù Hospital, Piazza S. Onofrio 4 00165, Rome, Italy.
    • ,
  • Roberta Iacobelli, MD

      Affiliations

    • Department of Cardiology, Bambino Gesù Pediatric Hospital, Rome, Italy
    • ,
  • Roberto M. Di Donato, MD

      Affiliations

    • Department of Cardiothoracic Surgery, Bambino Gesù Pediatric Hospital, Rome, Italy
    • American Association for Thoracic Surgery member.
    • ,
  • Francesca Raimondi, MD

      Affiliations

    • Department of Cardiology, Bambino Gesù Pediatric Hospital, Rome, Italy
    • ,
  • Adriano Carotti, MD

      Affiliations

    • Department of Cardiothoracic Surgery, Bambino Gesù Pediatric Hospital, Rome, Italy
    • ,
  • Vincenzo Di Ciommo, MD

      Affiliations

    • UO Epidemiology, Bambino Gesù Hospital, Rome, Italy
    • ,
  • Stephen P. Sanders, MD, FACC

      Affiliations

    • Department of Cardiology, Bambino Gesù Pediatric Hospital, Rome, Italy

Received 14 February 2008 ,Revised 2 July 2008 ,Accepted 11 August 2008.

References 

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  3. Shone JD, Sellers RD, Anderson RC, Adams P, Lillehei CW, Edwards JE. The developmental complex of “parachute mitral valve,” supravalvar ring to the left atrium, subaortic stenosis and coarctation of the aorta. Am J Cardiol. 1963;11:714–725
  4. Ruckman RN, Van Praagh R. Anatomic types of congenital mitral stenosis: report of 49 autopsy cases with consideration of diagnosis and surgical implications. Am J Cardiol. 1978;42:592–601
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  6. Serraf A, Zoghby J, Belli E, Lacour-Gayet F, Aznag H, Houyel L, et al. Congenital mitral stenosis with or without associated defects: an evolving surgical strategy. Circulation. 2000;102(19 suppl. 3):III166-71
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  12. Marino B, Sanders SP, Parness IA, Colan SD. Obstruction of right ventricular inflow and outflow in corrected transposition of the great arteries (SLL): two dimensional echocardiographic diagnosis. J Am Coll Cardiol. 1986;8:407–411
  13. Brauner RA, Laks H, Drinkwater DC, Scholl F, McCaffery S. Multiple left heart obstructions (Shone's anomaly) with mitral valve involvement: long-term surgical outcome. Ann Thorac Surg. 1997;64:721–729
  14. Coles JG, Williams WG, Watanabe T, Duncan KF, Sherret H, Dasmahapatra HK, et al. Surgical experience with reparative techniques in patients with congenital mitral valve anomalies. Circulation. 1987;76(3 Pt 2):III117–III122
  15. Aharon AS, Laks H, Drinkwater DC, Chugh R, Gates RN, Grant PW, et al. Early and late results of mitral valve repair in children. J Thorac Cardiovasc Surg. 1994;107:1262–1270
  16. Sullivan ID, Robinson PJ, de Leva IM, Graham TP. Membranous supravalvar mitral stenosis: a treatable form of congenital heart disease. J Am Coll Cardiol. 1986;8:159–164
  17. Collison SP, Kaushal SK, Dagar KS, Iyer PU, Girotra S, Radhakrishnan S, et al. Supramitral ring: good prognosis in a subset of patients with congenital mitral stenosis. Ann Thorac Surg. 2006;81:997–1001
  18. Moore P, Adatia I, Spevak PJ, Keane JF, Perry SB, Castaneda AR, et al. Severe congenital mitral stenosis in infants. Circulation. 1994;89:2099–2106
  19. Tulloh RM, Bull C, Elliott MJ, Sullivan ID. Supravalvar mitral stenosis: risk factors for recurrence or death after resection. Br Heart J. 1995;73:164–168
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  21. Brown JW, Ruzmetov M, Vijay P, Rodefeld MD, Turrentine MW. Surgery for aortic stenosis in children: a 40-year experience. Ann Thorac Surg. 2003;76:1398–1411

PII: S0022-5223(08)01416-5

doi: 10.1016/j.jtcvs.2008.08.023

The Journal of Thoracic and Cardiovascular Surgery
Volume 137, Issue 3 , Pages 538-542 , March 2009

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